PEDIATRICS MCQS: NEONATOLOGY

MCQS

MCQS#01

Which of the following syndromes is the most common cause of hypertrophic cardiomyopathy in neonates and children under age 4 years?

A. Apert syndrome

B. CHARGE association

C. Noonan syndrome

D. Trisomy 18

E. Turner syndrome

MCQS#02

A fetus at 20 weeks’ gestation is diagnosed with congenital heart block.

Which of the following statements about neonatal lupus erythematosus (NLE) is FALSE?

A.  Anti-SSA/Ro and anti-SSB/La antibodies are nearly universally found in the        serum of women whose fetuses are diagnosed in utero with congenital heart       block

B.  Complete congenital heart block is irreversible and surviving children                 typically   require pacing

C.  Congenital heart block resulting from NLE is typically diagnosed between 16       and 24 weeks’ gestation

D.  The majority of mothers of neonates diagnosed with congenital heart block         have symptoms of systemic lupus erythematosus

E.  The mortality rate of congenital heart block in NLE is approximately 20%

MCQS#03

You are called to the Delivery Room to evaluate a cyanotic term neonate. On arrival, you note a severely cyanotic female neonate without respiratory distress. The infant has 2+ distal pulses bilaterally, no murmur, and a loud, single S2. The chest radiograph shows a normal heart size and a narrow mediastinum. You contact a cardiologist and order intravenous prostaglandin therapy. An echocardiogram confirms the diagnosis.

What is the likely next step in the management of this infant?

A. Blalock-Taussig shunt procedure

B. Inhaled nitric oxide therapy

C. Jatene arterial switch procedure

D. Pulmonary artery banding

E. Rashkind balloon septostomy

MCQS#04

The patent ductus arteriosus (PDA) is considered to be a common form of congenital heart disease, with an incidence of about 1 per 2,000 live births.

Even if asymptomatic in childhood, an untreated PDA may cause all of the following EXCEPT:

A. Congestive heart failure

B. Endarteritis

C. Endocarditis

D. PDA aneurysm

E. Pulmonary hypertension

MCQS#05

During a routine physical examination, you hear a cardiac murmur in a 3-day old girl, the recipient of twins diagnosed prenatally with twin-to-twin transfusion syndrome (TTTS).

Which of the following statements about this scenario is TRUE?

A. Congenital heart defects are more prevalent in monochorionic infants with          TTTS.

B. The recipient twin is more frequently symptomatic.

C. There is a three-fold increase in the frequency of congenital heart defects.

D. Ventricular septal defects, atrial septal defects and pulmonary stenosis are         seen most frequently.

E.  All of the above are true

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