Answer to MCQS of the WEEK

Answer to MCQS of the WEEK

The child in the question likely has Kasabach-Merritt phenomenon, which is seen with large vascular anomalies (ie, Kaposiform hemangioendothelioma and tufted angioma). Platelet and RBC sequestration within the vascular tumor causes peripheral thrombocytopenia, coagulopathy, and microangiopathic hemolytic anemia. Treatment options include corticosteroids, α- interferon, and vincristine. Surgery frequently results in excessive bleeding.

Nevus simplex is a common minor vascular malformation seen on the glabella, eyelids, and nape of the neck in newborns; such lesions on the face are also called “angel or stork kiss,” while lesions on the back of the neck are called “stork bite.” 

Nevus flammeus, or port wine stain, is a large sharply demarcated pink to purple vascular malformation that can occur anywhere. Port wine stain involving the VI distribution of the trigeminal nerve should raise the suspicion of Sturge-Weber syndrome. 

PHACE(S) syndrome includes posterior fossa malformations, large facial hemangiomas, arterial abnormalities, coarctation of the aorta, eye abnormalities, and sternal defects. 

Infantile fibrosarcoma is a malignant congenital tumor that can be easily mistaken for an infantile hemangioma; a high index of suspicion is required to investigate further if a “hemangioma” is not resolving as expected.

Correct answer is 'a'